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Melorheostosis of spine: A very rare clinical entity
Jayprakash V Modi, Harshil R Patel
Department of Orthopedics, Civil Hospital, Ahmedabad, Gujarat, India
Correspondence Address:
Harshil R Patel,
5 Birva Row House, Near Bopal Gram Panchayat, Bopal, Ahmedabad-58, Gujarat.
India
 Source of Support: None, Conflict of Interest: None DOI: 10.4103/isj.isj_68_19
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Melorheostosis is a medical developmental disorder and mesenchymal dysplasia in which bone cortex widens and becomes hyperdense in a sclerotomal distribution. Most of the cases reported till now are confined to appendicular skeleton, rarely affecting spine. It is well known by its characteristic appearance of “melting wax flowing down a candle” on radiographs. Here we report a rare case of melorheostosis of thoracic spine in a middle-aged male patient with features of myelopathy treated by early decompression surgery, leading to complete relief of symptoms postoperatively. Final follow-up was of 2 years. It is a very rare, benign and disabling entity, and the diagnosis is primarily a radiological one. Early diagnosis and decompression surgery leads to dramatic improvement in clinical outcome and prevents unwarranted biopsy. |
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